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Título : Assessment of ataxia rating scales and cerebellar functional tests : critique and recommendations
Autor : Pérez Lloret, Santiago 
Warrenburg, Bart van de 
Rossi, Malco Damián 
Rodríguez-Blázquez, Carmen 
Zesiewicz, Theresa 
Saute, Jonas A. M. 
Durr, Alexandra 
Nishizawa, Masatoyo 
Martinez-Martin, Pablo 
Stebbins, Glenn T. 
Schrag, Anette 
Skorvanek, Matej 
Fecha de publicación : 2020
Editorial : Wiley
Cita : Pérez Lloret, S. [et al.]. Assessment of ataxia rating scales and cerebellar functional tests : critique and recommendations [en línea]. Movement Disorders. 2020. Disponible en:
Resumen : Background: We assessed the clinimetric properties of ataxia rating scales and functional tests, and made recommendations regarding their use. Methods: A systematic literature search was conducted to identify the instruments used to rate ataxia symptoms. The identified rating scales and functional ability tests were reviewed and ranked by the panel as “recommended,” “suggested,” or “listed” for the assessment of patients with discrete cerebellar disorders, using previously established criteria. Results: We reviewed 14 instruments (9 rating scales and 5 functional tests). “Recommended” rating scales for the assessment of symptoms severity were: for Friedreich’s ataxia, the Friedreich’s Ataxia Rating Scale, the International Cooperative Ataxia Rating Scale (ICARS), and the Scale for the Assessment and Rating of Ataxia (SARA); for spinocerebellar ataxias, ICARS and SARA; for ataxia telangiectasia: ICARS and SARA; for brain tumors, SARA; for congenital disorder of glycosylation-phosphomannomutase-2 deficiency, ICARS; for cerebellar symptoms in multiple sclerosis, ICARS; for cerebellar symptoms in multiple system atrophy: Unified Multiple System Atrophy Rating Scale and ICARS; and for fragile X–associated tremor ataxia syndrome, ICARS. “Recommended” functional tests were: for Friedreich’s ataxia, Ataxia Functional Composite Score and Composite Cerebellar Functional Severity Score; and for spinocerebellar ataxias, Ataxia Functional Composite Score, Composite Cerebellar Functional Severity Score, and SCA Functional Index.
ISSN : 1531-8257 (online)
Disciplina: MEDICINA
DOI: 10.1002/mds.28313
Derechos: Acceso abierto
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